Plexiform Neurofibroma

A type of neurofibroma manifesting as a diffuse overgrowth of subcutaneous tissue, usually involving the face, scalp, neck, and chest but occasionally occurring in the abdomen or pelvis. The tumors tend to progress, and may extend along nerve roots to eventually involve the spinal roots and spinal cord. This process is almost always a manifestation of NEUROFIBROMATOSIS 1. (From Adams et al., Principles of Neurology, 6th ed, p1016; J Pediatr 1997 Nov;131(5):678-82)

Also Known As:

Neurofibroma, Plexiform; Tumor Royale; Elephantiasis Neuromatoses; Neurofibromas, Plexiform; Neuroma, Plexiform; Pachydermatoceles; Plexiform Neurofibromas; Plexiform Neuroma; Plexiform Neuromas; Elephantiasis Neuromatosis; Neuromas, Plexiform; Pachydermatocele

Neoplasms: 1361496
- Neoplasms by Histologic Type: 2
  - Nerve Tissue Neoplasms: 1
    - Nerve Sheath Neoplasms: 280
      - Neurofibroma: 865
        Plexiform Neurofibroma: 282
Nervous System Diseases: 14737
- Neuromuscular Diseases: 2048
  - Peripheral Nervous System Diseases: 11768
    - Peripheral Nervous System Neoplasms: 49
      - Nerve Sheath Neoplasms: 280
        Neurofibroma: 865
        Plexiform Neurofibroma: 282
- Nervous System Neoplasms: 237
  - Peripheral Nervous System Neoplasms: 49
    - Nerve Sheath Neoplasms: 280
      - Neurofibroma: 865
        Plexiform Neurofibroma: 282

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